Biliary Papillomatosis: case report

Biliary papillomatosis is exceedingly rare. Only sporadic cases were reported since the first description of this disease by Caroli in 1959. The disease is characterized by multiple and recurrent papillary adenoma in the biliary tree. Jaundice and cholangitis are ususally the main presenting symptoms. Although biliary papillomatosis is generally considered a benign disease, varying degree of dysplastic change in the epithelium is always present and progression to malignancy has been reported. The disease ultimately leads to death from sepsis or liver failure. In this paper, we present a new patient of biliary papillomatosis and describe the imaging findings including sonography, CT scan, MRI and ERCP.